Primitive neuroectodermal tumor in a child with tuberous sclerosis

Research paper by Bernard W. Hindman, Harmandeep K. Gill, Craig W. Zuppan

Indexed on: 01 Mar '97Published on: 01 Mar '97Published in: Skeletal Radiology


The case of a 13-year-old boy with tuberous sclerosis and primitive neuroectodermal tumor of bone is presented. A pathogenetic association between these two entities is postulated, the unifying underlying mechanism being a maldevelopment of the neural crest, or neurocristopathy.