Bobble-head doll syndrome due to a suprasellar arachnoid cyst: endoscopic treatment in two cases.

Research paper by A A Fioravanti, U U Godano, A A Consales, C C Mascari, F F Calbucci

Indexed on: 02 Apr '04Published on: 02 Apr '04Published in: Child's Nervous System


We report two cases of bobble-head doll syndrome associated with a large suprasellar arachnoid cyst successfully treated with a minimally invasive endoscopic approach.The clinical history, surgical treatment and results of two children, a 9-year-old boy and a 1-year-old girl, both presenting the clinical features of the bobble-head doll syndrome, are described. As a first procedure, a ventriculo-cystostomy was endoscopically performed in both patients, obtaining either resolution of the symptoms or notable cyst reduction. In the girl, a re-closure of the stoma, with cyst re-expansion, was observed after 18 months. She then underwent a second procedure, a ventriculo-cysto-cisternostomy, with a good result. After 3 years' follow-up, the neurological condition of both patients remains good with complete resolution of abnormal head movement.In our opinion, endoscopic treatment is the procedure of choice for this condition, as it involves few complications and gives good results.