Atrialized right ventricular myxoma in a patient with Ebstein's anomaly.

Research paper by T J TJ John, H W HW Snyman, J J Janson, A J K AJK Pecoraro

Indexed on: 23 Feb '18Published on: 23 Feb '18Published in: Echo research and practice


Ebstein's anomaly is a rare entity affecting around 1 in 200,000 live births and accounts for less than 1% of congenital heart diseases. Ebstein's anomaly with an associated right-sided myxoma is extremely rare, with only one other case report found in the literature. Previous reports have also noted cases of Ebstein's anomaly associated with left-sided myxomas. We describe a female patient with, to our knowledge, the first case of a histopathologically confirmed right ventricular myxoma in the setting of Ebstein's anomaly. © 2018 The authors.