An enormous shunt between the portal and hepatic veins associated with multiple coronary artery fistulas

Research paper by K. Mori, T. Dohi, H. Yamamoto, M. Kamada

Indexed on: 01 Dec '90Published on: 01 Dec '90Published in: Pediatric Radiology


A 9-year-old boy with a rare combination of multiple coronary artery fistulas and congenital shunt between the portal and hepatic veins (portal-systemic shunt) is presented. The most likely pathogenesis for the portal-systemic shunt in this case was persistence of the ductus venosus as a bypass tract of the portal vein. This shunt is considered as one cause of cardiomegaly and dilatation of the hepatic vein in this case, and careful follow-up is mandatory because this shunt could induce, portal-systemic encephalopathy.